Snapshot hematology

Preparation of slides
- centrifugated (in Dutch: gespind) +: equal distribution -: need a lot of work
- smear -: not equal distribution (overestimation neutrophils, underestimation lymphocytes).

- Standard stain: Grunwald

Workflow
- fluorescense identification of the blood cells, automated flagging system using (for example using Cell Dyne Sapphire, Abbott).
   - reactive cells: zone between lymphocytes and monytes
- smear

Two types
- bone marrow: various stadia
- peripheral

Morphology of the cells
- immature granulocytes: myelocyte, metamyelocyte

- monocytes: granular

- reactive neutrophils: large granulocytes, vacuolisation, a lot of young

- eosinophils: orange

- lymphocytes: empty cytoplasm,
   - B/T cells: reactive vs. malignant
   - atypical lymphocytes (reactive, not malignant)
      for example in mononucleosis
   - plasma cells --> plasmocytes
      - blue border
      - large nucleus: not yet turned into plasma cells

- erythrocytes
   - erythroblasts: nucleated red blood cells, blue (polychromasie: rest of DNA)
   - cold vs. warm agglutination. Mostly cold. (vs. Cryoglubulinel: humoral).

- thrombocytes
  - ITP: few megakaryocytes, platelets are as big as RBCs
  - trombocytes aggregation: problem with blood withdrawal (fibrin can be also seen), EDTA tube problem (less with citrate).

Morphology of the diseases
Anemia
- Microcytaire hympchrom anemia
   - small erythrobalsts
   - also in chronic infection

- Pernicious
   - big oval RBC (macrocytes)
   - not too many RBCs
   - also: hypersegmentation neutrophils,
   - problem with DNA production

- Thalassemia
   - mostly Beta minor in Belgium
   - poikilocytosis (pear like), target cells, basophilic stippling (also in lead poisoning).

- Sickle cell (SCD)
   - homozygotes mutation that produces HbS (can be seen on electrophoresis), 30% in SCD
   - target cells, Howell Jolly body RBCs (cluster DNA remnants, indicates spleen damage)
   - also: large platelets

- G6PD
   - can be triggered by medication for example antimalarial
   - unstable hb
   - blister cells (bite cells)
 
- increased hemolysis
   - small RBCs with hole, normal Hb, increased MCHC
 
- autoimmune hemolysis
  - spherocytes, polychromasie, increased reticulocytes (young RBCs).

- microangiopathic hemolysis (HUS, TTP)
   - Von Willebrand factor deficiency
   - helmet cells/ schistocytes (small part of RBCs is 'bitten'): mechanical breakdown against fibrine.
      Helmet cells are better visualized using smeared using Grunwald stain than spinned
   - low platelets
    - increased ureum
   - HUS: bloody diarrhea

Malignanacy
- the diagnosis is in bone marrow
- myelopriliferative (still functional)  vs. myelodysplasia (not functional, a lost of blasts)

- Chronic myeloid leukemia
   - not a precise term, actually is not a leukemia, it is myeloproliferative
   - granulocytes proliferation

- polycythemia vera (Vaquez disease)
  - 5 to 10% RBCs

- Essential trombocytosis
  - 1 to 10% peripheral thrombocytes

- Myelofibrosis
  - Fibroblasts, erythroblasts, tear drop, immature granulocytes, empty bone marrow,
  - extramedullair take it over: enlarge liver and spleen

- Myelodysplastic
   - refractaire anemia with ringed sideroblasts --> precursor of leukemia
   - unilineage RBC (with sideroblasts), multilineage
   - hypogranulation

- Leukemia
   - blasts proliferation
   - monoclonal
   - lymphatic or myeloid
   - emergency (on call)
   - AML
      - myeloblasts (fine granulocytes)
      - Auers rods (in AML, primary granulocytes fused, peroxidase stain)
      - AML: M1 to M7 using FAB classification
   - ALL
     - no peroxidase, cleavage, no cytoplasm, vacuoles
     - perform phenotyping
     - red sign: trombocytopenia, and pancytopenia
   - Myelomas
     - monoclonal plasma cells
     - plasma cells leukemia when it is peripheral
     - RBCs train: heavy protein, increased ESR (due to fibrinogen, versus reactive plasma cells)
   - Lymphomas
      - Non Hodgkin
      - mostly B cells
      - monoclonal
   - CLL
      - lymphocytosis
      - mature B cells from blood as origin (vs. lymph node in NHL)
      - atypical lymphocytes (can also be reactive)
      - T cells > B cells
      - centrocytes, cleaved, like paint on the ground
  - Hairy cell leukemia
     - is visualized better in smeared not spinned
     - from the milt
    

Geen opmerkingen:

Een reactie posten